Allgrove Syndrome (AAA Syndrome): Case Report of Dental Management of 15 Years Old Male

Muhammada  Zainab; Shahzad  Nasir; Hassan  Shahzad

doi:10.36283/ziun-pjmd14-4/106

Authors

Muhammada Zainab Margalla Institute of Health Sciences, Rawalpindi, Pakistan. https://orcid.org/0009-0005-6101-163X
Shahzad Nasir Margalla Institute of Health Sciences, Rawalpindi, Pakistan. https://orcid.org/0009-0001-2670-7624
Hassan Shahzad Margalla Institute of Health Sciences, Rawalpindi, Pakistan. https://orcid.org/0009-0001-9614-3721

DOI:

https://doi.org/10.36283/ziun-pjmd14-4/106

Keywords:

Allgrove Syndrome, Triple A syndrome , ACTH resistant adrenal insufficiency, achalasia , alacrima, AAA Syndrome, Dental Management

Abstract

Allgrove Syndrome, also known as Triple A Syndrome, is a rare autosomal recessive multiorgan dysfunction. It is characterised by the three ‘A’s’ [hence the name]: Alacrima (a reduced or absent ability to secrete tears), Achalasia (absence of esophageal muscle peristalsis), and Adrenal insufficiency (Addison’s disease). About 1/3^rdof the patients present with neurological and autonomic manifestations including gait disturbances, parkinsonism, muscle weakness, mental retardation and peripheral sensory and motor neuropathy.

Here, we report a case of a 15-year-old male who had multiple carious teeth and broken down roots. The patient was first diagnosed at the age of 5 years and had a history of absence of tears, difficulty in swallowing and was on exogenous steroids. Patient had come to the Oral Surgery Department with the complaint of continuous, severe, nocturnal pain in the lower right 1st molar for the last 1 week. So, we doubled the dose of steroids as per protocol and extracted the tooth the following day.

Author Biographies

Muhammada Zainab, Margalla Institute of Health Sciences, Rawalpindi, Pakistan.

Department of Medical Education and Demonstrator,
Shahzad Nasir, Margalla Institute of Health Sciences, Rawalpindi, Pakistan.

Department of Oral & Maxillofacial Surgery and Assistant Professor,
Hassan Shahzad, Margalla Institute of Health Sciences, Rawalpindi, Pakistan.

Department of Community Dentistry and Demonstrator,

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